immunoproliferative small intestine disease (ipsid): a case report

نویسندگان

farid imanzadeh professor of children gastroenterology, gastroenterology unit, mofid hospital, shahid beheshti university of medical sciences, tehran, iran.

aliakbar sayarri professor of children gastroenterology, gastroenterology unit, mofid hospital, shahid beheshti university of medical sciences, tehran, iran.

pantea tajik fellow of children gastroenterology, gastroenterology unit, mofid hospital, shahid beheshti university of medical sciences, tehran, iran.

چکیده

immunoproliferative small intestinal disease (ipsid) is the syndrome associated with mediterranean lymphoma (a rare form of non-hodgkin’s lymphoma). many of the patients diagnosed with secretory ipsid have variable level of abnormal immunoglobulins in serum or other bodily fluids, identified as truncated alpha heavy chain globulins. most cases are characterized by a loss of ability to synthesize light chains. as such, ipsid has been classified as a heavy chain disorder b-cell lymphoma. we present here the case of a 12-year-old boy admitted in our department for edema, abdominal pain and ftt, in whom we suspected the diagnosis of ipsid.

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عنوان ژورنال:
international journal of pediatrics

جلد ۳، شماره ۲.۱، صفحات ۸۹-۹۲

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